Congenital cystic adenomatoid malformation type I

  • Alice Rebelo de Matos Borges dos Reis Department of Pathology - Faculty of Medicine - Universidade de São Paulo, São Paulo/SP
  • Frederico Becker Ribeiro Department of Pathology - Faculty of Medicine - Universidade de São Paulo, São Paulo/SP
  • Regina Schultz Department of Pathology - Faculty of Medicine - Universidade de São Paulo, São Paulo/SP
Keywords: Cystic Adenomatoid Malformation of Lung, Congenital, Classification, Prognosis, Autopsy

Abstract

Congenital cystic adenomatoid malformation (CCAM) is an hamartomatous congenital pulmonary airway malformation with incidence ranging between 1:10,000 and 1:35,000 newborns. Currently CCAM is classified into five groups according to clinical and pathological features. The clinical outcome varies depending on the subtype and the extent of involvement. The authors report the case of a premature male newborn with the prenatal diagnosis of CCAM Type 1 associated with cardiac right axis deviation, who died 67 hours after birth due to respiratory failure. In addition to the autopsy report of this rare entity, the authors present its classification and prognosis.

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Published
2015-09-28
How to Cite
Reis, A., Ribeiro, F., & Schultz, R. (2015). Congenital cystic adenomatoid malformation type I. Autopsy and Case Reports, 5(3), 21-26. Retrieved from http://www.revistas.usp.br/autopsy/article/view/107015
Section
Article / Autopsy Case Report