Fatal pulmonary thromboembolism associated with hemoglobin SC disease in a 15 year-old boy

Authors

  • Thiago Trolez Amancio Departamento de Patologia da Faculdade de Medicina da USP
  • Anderson da Costa Lino Costa Departamento de Patologia da Faculdade de Medicina da USP
  • Marcela Longo Borsato Departamento de Patologia da Faculdade de Medicina da USP
  • Leandro Marins Departamento de Patologia da Faculdade de Medicina da USP
  • Lívia Moscardi Bacchi Departamento de Patologia da Faculdade de Medicina da USP
  • Maria Claudia Nogueira Zerbini Serviço de Anatomia Patológica do Hospital Universitário da USP

DOI:

https://doi.org/10.4322/acr.%25y.26063

Keywords:

Autopsy, Hemoglobin SC disease, Thromboembolism, Sickle hemoglobin.

Abstract

We report a case of hemoglobin SC disease complicated by fatal pulmonary
thromboembolism in a 15 year-old Brazilian boy, submitted to autopsy. This
case shows the importance of early diagnosis and treatment of sickle cell
disease, which generates systemic involvement in youth and the importance
of considering the hypercoagulability in these patients. The autopsy was very
instructive, revealing the florid morphologic aspect of sickle cell disease and
its complications.

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Published

2011-09-29

Issue

Section

Article / Autopsy Case Report

How to Cite

Amancio, T. T., Costa, A. da C. L., Borsato, M. L., Marins, L., Bacchi, L. M., & Zerbini, M. C. N. (2011). Fatal pulmonary thromboembolism associated with hemoglobin SC disease in a 15 year-old boy. Autopsy and Case Reports, 1(3), 15-22. https://doi.org/10.4322/acr.%y.26063