Idiopathic sclerosing encapsulating peritonitis: an uncommon cause of intestinal obstruction

Authors

  • José de Arimatéia Batista Araújo Filho Heart Institute – Hospital das Clínicas – Faculdade de Medicina – Universidade de São Paulo
  • João Augusto Santos Martines Diagnostic Imaging Service – Hospital Universitário – Universidade de São Paulo
  • Brenda Margatho Ramos Martines Diagnostic Imaging Service – Hospital Universitário – Universidade de São Paulo
  • Adriano Ferreira Silva Diagnostic Imaging Service – Hospital Universitário – Universidade de São Paulo
  • Silvana Maria Lovisolo Anatomic Pathology Service – Hospital Universitário – Universidade de São Paulo
  • Cláudio Campi de Castro Diagnostic Imaging Service – Hospital Universitário – Universidade de São Paulo; Department of Radiology – Faculdade de Medicina – Universidade de São Paulo

DOI:

https://doi.org/10.4322/acr.%25y.48232

Keywords:

Abdominal pain, Intestinal obstruction, Peritoneal fibrosis, Surgery

Abstract

Sclerosing encapsulating peritonitis (SEP), also called encapsulating peritonitis, is a rare and benign cause of intestinal obstruction of unknown etiology. Its onset may be acute or subacute although there are some reports with a two-month history. More commonly, this entity is secondary to chronic peritoneal dialysis, ventriculoperitoneal and peritoneovenous shunting, the use of β-blockers and systemic lupus erythematous. Recurrent episodes of bacterial peritonitis, intestinal tuberculosis, sarcoidosis, familial Mediterranean fever, gastrointestinal cancer, liver transplantation, intra-abdominal fibrogenic foreign bodies, and luteinized ovarian thecomas are also related to SEP. The idiopathic presentation is more rare. Abdominal pain, nausea, vomiting, weight loss, malnutrition, and clinically palpable mass characterize the clinical features. Diagnosis is frequently made with gross findings during surgery, imaging workup and histopathology. The authors report the case of a 36-yearold male patient with a 10-day history of abdominal pain that was operated on because of intestinal obstruction. Diagnosis was made preoperatively and confirmed by the intraoperative findings and histopathology.

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Published

2012-09-09

Issue

Section

Article / Clinical Case Report

How to Cite

Idiopathic sclerosing encapsulating peritonitis: an uncommon cause of intestinal obstruction. (2012). Autopsy and Case Reports, 2(3). https://doi.org/10.4322/acr.%y.48232