Pulmonary agenesis and respiratory failure in childhood

Authors

  • Paula Vanessa Valverde Dinamarco Office of the Chief Medical Examiner, Santos/SP
  • Cesar Cilento Ponce Office of the Chief Medical Examiner, Santos/SP

DOI:

https://doi.org/10.4322/acr.%25y.98453

Keywords:

Lung agenesis, Respiratory Insufficiency, Autopsy

Abstract

Pulmonary agenesis (PA) is a rare congenital anomaly, which may be unilateral or bilateral. Unilateral PA may be associated with nonspecific respiratory symptoms. We report the case of 5-month-old infant who presented a normal development until the age of 4 months when a respiratory infection caused an acute respiratory distress syndrome with a fatal outcome. The autopsy findings depicted the right lung agenesis without any other concomitant malformation. Although respiratory symptoms represent frequent complaints in pediatrics, the aim of this study is not only to draw attention to the unilateral pulmonary agenesis as a possible underlying malformation in children who present recurrent and severe respiratory symptoms, but also to report a case diagnosed at autopsy.

Downloads

Download data is not yet available.

Downloads

Published

2015-03-31

How to Cite

Dinamarco, P. V. V., & Ponce, C. C. (2015). Pulmonary agenesis and respiratory failure in childhood. Autopsy and Case Reports, 5(1), 29-32. https://doi.org/10.4322/acr.%y.98453

Issue

Section

Article / Autopsy Case Report