Congenital cystic adenomatoid malformation type I

Authors

  • Alice Rebelo de Matos Borges dos Reis Department of Pathology - Faculty of Medicine - Universidade de São Paulo, São Paulo/SP
  • Frederico Becker Ribeiro Department of Pathology - Faculty of Medicine - Universidade de São Paulo, São Paulo/SP
  • Regina Schultz Department of Pathology - Faculty of Medicine - Universidade de São Paulo, São Paulo/SP

Keywords:

Cystic Adenomatoid Malformation of Lung, Congenital, Classification, Prognosis, Autopsy

Abstract

Congenital cystic adenomatoid malformation (CCAM) is an hamartomatous congenital pulmonary airway malformation with incidence ranging between 1:10,000 and 1:35,000 newborns. Currently CCAM is classified into five groups according to clinical and pathological features. The clinical outcome varies depending on the subtype and the extent of involvement. The authors report the case of a premature male newborn with the prenatal diagnosis of CCAM Type 1 associated with cardiac right axis deviation, who died 67 hours after birth due to respiratory failure. In addition to the autopsy report of this rare entity, the authors present its classification and prognosis.

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Published

2015-09-28

Issue

Vol. 5 No. 3 (2015)

Section

Article / Autopsy Case Report

License

Authors of articles published by Autopsy and Case Report retain the copyright of their work without restrictions, licensing it under the Creative Commons Attribution License - CC-BY, which allows articles to be re-used and re-distributed without restriction, as long as the original work is correctly cited.

How to Cite

Reis, A. R. de M. B. dos, Ribeiro, F. B., & Schultz, R. (2015). Congenital cystic adenomatoid malformation type I. Autopsy and Case Reports, 5(3), 21-26. https://www.revistas.usp.br/autopsy/article/view/107015