Medical considerations in the dental treatment of patients with Williams-Beuren syndrome - report of four clinical cases

Authors

  • Natália Silva Andrade University of São Paulo. School of Dentistry. Department of Stomatology
  • Cíntia Santos University of São Paulo. School of Dentistry. Department of Stomatology
  • Talita Castro University of São Paulo. School of Dentistry. Department of Stomatology
  • Marina Gallottini University of São Paulo. School of Dentistry. Department of Stomatology

DOI:

https://doi.org/10.11606/issn.2357-8041.clrd.2015.118463

Keywords:

Williams Beuren syndrome, Dental management, Heart diseases

Abstract

Williams-Beuren syndrome (WBS) is a rare genetic disorder characterized by peculiar facies, eyes, dental, cardiovascular, renal, and skeletal abnormalities, mental retardation, friendly and loquacious personality, and occasionally hypercalcemia in infancy. The orofacial aspects and especially the dental management of these patients have received little attention in the literature. The aim of this manuscript is to describe four cases of patients with WBS attended at Special Care Dentistry Center, School of Dentistry, University of São Paulo, with emphasis on the oral findings and systemic conditions of dental interest. The clinical management of patients with WBS is discussed. We conclude that congenital heart defects and behavioral changes are the aspects that most interfere on dental treatment

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Author Biographies

  • Natália Silva Andrade, University of São Paulo. School of Dentistry. Department of Stomatology

    Discipline of Oral Pathology, Department of Stomatology, School of Dentistry, University of São Paulo

  • Cíntia Santos, University of São Paulo. School of Dentistry. Department of Stomatology
    Discipline of Oral Pathology, Department of Stomatology, School of Dentistry, University of São Paulo
  • Talita Castro, University of São Paulo. School of Dentistry. Department of Stomatology
    Discipline of Oral Pathology, Department of Stomatology, School of Dentistry, University of São Paulo
  • Marina Gallottini, University of São Paulo. School of Dentistry. Department of Stomatology
    Discipline of Oral Pathology, Department of Stomatology, School of Dentistry, University of São Paulo

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Published

2015-12-26

Issue

Section

Case report or technical report