Impact of the motor function of individuals with spinal muscular atrophy on the overload of their caregivers
DOI:
https://doi.org/10.1590/1809-2950/e23003023ptKeywords:
Neuromuscular Disease, Rare Diseases, Caregiver BurdenAbstract
Spinal Muscular Atrophy (SMA) is a
neurodegenerative disease that impairs motor function,
justifying the help of a caregiver. This study aimed to analyze
the impact of the motor function of individuals with SMA
on caregiver burden. This is a cross-sectional study of 32
individuals with SMA and 27 caregivers, carried out in a
rehabilitation center, using the identification questionnaire,
anamnesis and sociodemographic profile, Motor Function
Measurement Scale and Burden Interview. Motor function
and caregiver burden were compared between SMA types
using the analysis of covariance (ANCOVA) and correlated
using Pearson’s correlation test. Individuals with SMA type I
had greater impairment of motor function when compared
to types II and III, and individuals with type III had better
scores in all domains of motor function. No correlation was observed between motor function and caregiver burden: however,
most caregivers presented some level of burden, especially those
from mild to moderate. Moderate to severe burden was found in
caregivers with SMA in a considerable prevalence, which requires
care and attention from health professionals.
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Copyright (c) 2023 Natália Guimarães Melo, Geovane Balçanufo de Souza e Silva, Cecília Rosa de Ávila, Francine Aguilera Rodrigues da Silva, Maysa Ferreira Martins Ribeiro, Letícia de Araújo Morais
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