Esclerose lateral amiotrófica em Belo Horizonte, Brasil entre 2010 e 2020: um estudo clínico epidemiológico

Autores

  • Myllena Harriman Faculdade Ciências Médicas de Minas Gerais https://orcid.org/0000-0002-0641-0532
  • Lucas Carneiro Morais Faculdade Ciências Médicas de Minas Gerais
  • Bruno Porto Pessoa Faculdade Ciências Médicas de Minas Gerais
  • Janaine Cunha Polese Faculdade Ciências Médicas de Minas Gerais https://orcid.org/0000-0003-3366-1545

DOI:

https://doi.org/10.11606/issn.2317-0190.v29i4a199833

Palavras-chave:

Esclerose Amiotrófica Lateral, Fatores Epidemiológicos, Estudo Clínico, Brasil

Resumo

Objetivo: Descrever o perfil clínico de indivíduos com Esclerose Lateral Amiotrófica (ELA) de um hospital de referência na cidade de Belo Horizonte, Brasil. Métodos: Trata-se de um estudo transversal retrospectivo com coleta de dados de prontuários eletrônicos de indivíduos com diagnóstico definido de ELA entre 2010 e 2020, no setor de referência em Distrofias Musculares de um hospital de uma capital brasileira. Resultados: Foram incluídos 103 indivíduos com ELA, com idade média de 60±12 anos, idade média de diagnóstico de 56±12 anos e tempo médio de evolução da doença de 3±3 anos. Além disso, 70% eram do sexo masculino, 88% com ELA esporádica, com envolvimento bulbar semelhante entre leve (32%), moderado (27%) e grave (28%), e com maior taxa de diagnóstico de 50 a 70 anos de idade. Conclusão: Os dados epidemiológicos deste estudo são muito semelhantes aos da literatura. No entanto, a heterogeneidade da doença, a complexidade do diagnóstico e a diversidade de formas que cada estudo traz para a doença, e principalmente a rápida progressão, dificultam a discussão de um quadro mais extenso. Traçar esse perfil é importante para uma clínica mais focada e um manejo mais adequado, e para isso são necessários mais estudos.

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Publicado

2022-12-28

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1.
Harriman M, Carneiro Morais L, Porto Pessoa B, Polese JC. Esclerose lateral amiotrófica em Belo Horizonte, Brasil entre 2010 e 2020: um estudo clínico epidemiológico. Acta Fisiátr. [Internet]. 28 de dezembro de 2022 [citado 3 de março de 2024];29(4):245-50. Disponível em: https://www.revistas.usp.br/actafisiatrica/article/view/199833

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